Presented by:
Nader ALDAjani
Otologist, KFMC
Definition:
- Misnomer; neither contains cholesterol crystals nor is a tumor.
- Skin in the wrong place.
Pathophysiology:
- Squamous epithelium in the middle ear or mastoid.
- Desquamation leads to keratin debris accumulation.
- Associated with bone and soft tissue erosion and recurrent infections.
Types:
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Acquired:
- Primary: Due to invagination of a retraction pocket. - associated with negative ear pressure (eustachian tube dysfunction).
- Secondary: Ingrowth of keratinizing epithelium into the middle ear space through a pre-existing TM perforation.
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Congenital:
- Presents as a white mass generally in the anterosuperior middle ear with an intact TM.
- Presents as a white mass generally in the anterosuperior middle ear with an intact TM.
Presentation:
- Progressive conductive hearing loss (CHL), discharge. ((cholesteatoma can act as a sound conductor))
- OE: White “pearly” mass, perforation, discharge, polyps, destruction of attic area.
- Tests: CT, PTA, Tympanometry.
congenital if there are no perforations
Complications:
- Destruction of the ossicular chain.
- Chronic otitis media.
- Labyrinthine fistula.
- Intracranial complications.
- Facial nerve paralysis.
Management:
Antibiotics.
Surgery.
- Aim: to remove the disease, restore the function.
- Mastoidectomy.
- Reconstructive surgery.
Tympanoplasty & Mastoidectomy
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Tympanoplasty: Surgical reconstruction of the tympanic membrane.
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Mastoidectomy: Surgical procedure to remove infected mastoid air cells.