Presented by:

Nader ALDAjani
Otologist, KFMC

Definition:

  • Misnomer; neither contains cholesterol crystals nor is a tumor.
  • Skin in the wrong place.

Pathophysiology:

  • Squamous epithelium in the middle ear or mastoid.
  • Desquamation leads to keratin debris accumulation.
  • Associated with bone and soft tissue erosion and recurrent infections.

Types:

  1. Acquired:

    • Primary: Due to invagination of a retraction pocket. - associated with negative ear pressure (eustachian tube dysfunction).
    • Secondary: Ingrowth of keratinizing epithelium into the middle ear space through a pre-existing TM perforation.
  2. Congenital:

    • Presents as a white mass generally in the anterosuperior middle ear with an intact TM.

Presentation:

  • Progressive conductive hearing loss (CHL), discharge. ((cholesteatoma can act as a sound conductor))
  • OE: White “pearly” mass, perforation, discharge, polyps, destruction of attic area.
  • Tests: CT, PTA, Tympanometry.

congenital if there are no perforations

Complications:

  • Destruction of the ossicular chain.
  • Chronic otitis media.
  • Labyrinthine fistula.
  • Intracranial complications.
  • Facial nerve paralysis.

Management:

Antibiotics.

Surgery.

  • Aim: to remove the disease, restore the function.
  • Mastoidectomy.
  • Reconstructive surgery.

Tympanoplasty & Mastoidectomy

  • Tympanoplasty: Surgical reconstruction of the tympanic membrane.

  • Mastoidectomy: Surgical procedure to remove infected mastoid air cells.

http://www.ghorayeb.com/mastoidectomy.html