Ischemic Optic Neuropathy

  • Two forms of ischemic optic neuropathy are:

    • Non-Arteritic (NAION) 95%

    • Arteritic (AAION). 5%

  • The main cause of AAION is vasculitis of the short posterior ciliary vessels supplying the optic nerve head.

  • large multinucleated monocytes infiltrate the small- and medium-sized arteries, causing obliteration of their lumen leading to ischemia.

Symptomatology:

AAION:

  • Mean age of onset: 70 years
  • Headache is the most common symptom.
  • Rheumatic myalgia (poly myalgia rheumatica)
  • Scalp tenderness
  • Jaw claudication
  • Malaise, anorexia, weight loss, low-grade fever
  • Severe visual loss, developing over hours to days.
  • Pallid disc edema (chalky white appearance of the disc)
  • Disc of fellow eye: normal



NAION

  • Cause of NAION:

    • Hypoperfusion or Non-perfusion of the optic nerve head.
  • Risk factors of NAION:

    • Diabetes mellitus
    • Hypertension
    • Hypercholesterolemia
    • Smoking

Symptomatology:

  • Mean age of onset: 60 years
  • Patients present with Painless vision loss developing over hours to days.
  • Visual loss is less severe than AAION.
  • No systemic symptoms.

Signs:

  • Segmental or diffuse disc swelling, hyperemic or pale.
  • Peripapillary retinal hemorrhages.
  • Disc in fellow eye “disc at risk”: small, crowded, elevated with blurry margin

  • Management:
    • AAION

      • It is life and vision-threatening.
      • High-dose (steroid) oral prednisone or intravenous methyl-prednisolone followed by a course of oral prednisone.
    • NAION:

      • No proven treatment
      • Optimize the medical condition.